Malformação adenomatoide cística tipo i: relato de caso e revisão bibliográfica

Abstract

Cystic adenomatoid malformation (CAM) is an abnormality of lung development resulting from the abnormal growth of the terminal respiratory bronchioles.As it is a rare malformation, lack of knowledge has been responsible for a late diagnosis. Advances in diagnostic imaging have contributed to increased detection of lesions, both pre and postnatal. CAM is classified into five types in relation to pathological conditions and lesion size, from which the clinical/prognostic repercussions derive.The present study describes the clinical case of a child born at the University Hospital of the Federal University of Grande Dourados (HU-UFGD) in July 2020 and diagnosed with type I cystic adenomatoid malformation. Initially at admission, she had respiratory distress syndrome, which evolved with drops in saturation and oxygen dependence. After performing Computed Tomography, multiple diffuse cystic images were shown in the left lung, suggesting MAC. The patient underwent surgery for upper left lobectomy, and in the postoperative period she presented clinical complications, but due to her improvement and stability, she was discharged twenty-seven days after the lobectomy, having been followed up in pediatrics at the Infant Care Emergency Room. It was concluded that it is important for pediatricians to expand diagnostic investigations, especially of congenital entities, as soon as recurrences of respiratory distress and pulmonary infections appear.